| 产品详情 |
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| Product Name | ADSL, Recombinant, Human, aa1-484, His-Tag |
| Description | Purity ~95% (SDS-PAGE). ADSL, is an enzyme that converts adenylosuccinate to AMP and fumarate as part of the purine nucleotide cycle. Defects in ADSL are the cause of adenylosuccinase deficiency (ADSL deficiency). ADSL deficiency is an autosomal recessive disorder characterized by the accumulation in the body fluids of succinylaminoimidazole-carboxamide riboside (SAICA-riboside) and succinyladenosine (S-Ado). Source: Recombinant corresponding to aa1-484 from human ADSL, fused to His-tag at N-terminal expressed in E.coli. AA Sequence: MRGSHHHHHH GMASMTGGQQ MGRDLYDDDD KDRWGSMAAG GDHGSPDSYR SPLASRYASP EMCFVFSDRY KFRTWRQLWL WLAEAEQTLG LPITDEQIQE MKSNLENIDF KMAAEEEKRL RHDVMAHVHT FGHCCPKAAG IIHLGATSCY VGDNTDLIIL RNALDLLLPK LARVISRLAD FAKERASLPT LGFTHFQPAQ LTTVGKRCCL WIQDLCMDLQ NLKRVRDDLR FRGVKGTTGT QASFLQLFEG DDHKVEQLDK MVTEKAGFKR AFIITGQTYT RKVDIEVLSV LASLGASVHK ICTDIRLLAN LKEMEEPFEK QQIGSSAMPY KRNPMRSERC CSLARHLMTL VMDPLQTASV QWFERTLDDS ANRRICLAEA FLTADTILNT LQNISEGLVV YPKVIERRIR QELPFMATE |
| Size | 100ug, 500ug |
| Concentration | n/a |
| Applications | n/a |
| Other Names | ADSL, Recombinant, Human, aa1-484, His-Tag (Adenylosuccinate Lyase, Adenylosuccinase, ASase, ASL, AMPS) |
| Gene, Accession, CAS # | Accession: NP_000017 |
| Catalog # | A0909-60E |
| Price | |
| Order / More Info | ADSL, Recombinant, Human, aa1-484, His-Tag from UNITED STATES BIOLOGICAL |
| Product Specific References | n/a |
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