产品详情 |
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Antigenic Specificity | DBT |
Clone | polyclonal |
Host Species | Rabbit |
Reactive Species | human, mouse, rat |
Isotype | n/a |
Format | purified |
Size | 100 µL |
Concentration | n/a |
Applications | Immunocytochemistry: 1:100-1:1000, Immunofluorescence: 1:100-1:1000, Immunohistochemistry (Paraffin): Assay-Dependent, Western Blot: 1:500-1:3000 |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | DBT Polyclonal Antibody. The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. |
Immunogen | n/a |
Other Names | BCATE2, E2, E2B, BCKAD E2 subunit, BCKAD-E2, BCKADE2, E2 component of branched chain alpha-keto acid dehydrogenase complex, branched chain acyltransferase, E2 component, branched-chain alpha-keto acid dehydrogenase complex component E2, dihydrolipoamide acetyltransferase compon |
Gene, Accession # | Entrez: 13171, 1629, 29611; Uniprot: P11182, P53395 |
Catalog # | PA5-29727 |
Price | |
Order / More Info | DBT Antibody from INVITROGEN ANTIBODIES |
Product Specific References | n/a |
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