产品详情 |
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Antigenic Specificity | ACAT1 |
Clone | monoclonal |
Host Species | Mouse |
Reactive Species | human |
Isotype | IgG1,k |
Format | purified |
Size | 100ul, 50ul |
Concentration | n/a |
Applications | ELISA, WB, ICC/IF |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | ACAT1 (acetyl-Coenzyme A acetyltransferase 1) is a 417 amino acid protein. ACAT1 is a mitochondrial enzyme involved in the formation and degradation of ketone bodies and is necessary for the proper metabolic processing of isoleucine. ACAT1 and ACAT2 catalyze the formation of acetoacetyl-CoA from two acetyl-CoA molecules. These enzymes are also capable of the reverse reaction. Defects in ACAT1 are a cause of 3-ketothiolase deficiency. 3-ketothiolase deficiency is an inborn error of isoleucine catabolism characterized by intermittent ketoacidotic attacks associated with unconsciousness. Some patients die during an attack or are mentally retarded. |
Immunogen | Recombinant human ACAT1 (34-427aa) purified from E. coli |
Other Names | acetyl-CoA acetyltransferase 1, ACAT, MAT, T2, THIL |
Gene, Accession # | NP 000010 |
Catalog # | ATGA0240 |
Price | |
Order / More Info | ACAT1 Antibody from ATGen |
Product Specific References | n/a |
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