产品名称 ACY1 Antibody from ATGen
产品货号 ATGA0329
产品价格 现货询价,电话:010-67529703
产品规格 100ul, 50ul
产品品牌 ATGen
产品概述
产品详情
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Antigenic SpecificityACY1
Clonemonoclonal
Host SpeciesMouse
Reactive Specieshuman
IsotypeIgG2b,k
Formatpurified
Size100ul, 50ul
Concentrationn/a
ApplicationsELISA, WB, Flow cytometry, ICC/IF
Reviews / RatingsIf you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY.
DescriptionAminoacylase-1, also designated N-acyl-L-amino-acid amidohydrolase or ACY1, is a member of the largest metallopeptidase family called M20A. Aminoacylase-1 is a zinc-binding homodimeric enzyme expressed in kidney, brain, placenta and spleen. It is the most abundant of the aminoacylases. Defects in ACY1 are the cause of aminoacylase-1 deficiency (ACY1D). ACY1D results in a metabolic disorder manifesting with encephalopathy, unspecific psychomotor delay, psychomotor delay with atrophy of the vermis and syringomyelia, marked muscular hypotonia or normal clinical features. All affected individuals exhibit markedly increased urinary excretion of several N-acetylated amino acids.
ImmunogenRecombinant human ACY1 (1-408aa) purified from E. coli
Other NamesAminoacylase 1, ACY1D, ACYLASE, Aminoacylase 1
Gene, Accession #NP 000657
Catalog #ATGA0329
Price
Order / More InfoACY1 Antibody from ATGen
Product Specific Referencesn/a
产品资料